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Pseudomyxoma retroperitonei with spontaneous skin fistula
1Department of Radiology, National Defense Medical College, 3-2, Tokorozawa-city, Saitama Prefecture 359, Japan.
Abstract:
We describe the imaging features in a patient with pseudomyxoma retroperitonei arising from a mucinous carcinoma of the appendix with spontaneous development of a skin fistula. The thick wall and septa characteristic of pseudomyxoma were best demonstrated on gadolinium-enhanced magnetic resonance imaging. This patient illustrates (a) the potential of pseudomyxoma to cause skin fistula and (b) the possibility that this intraabdominal process can first present as a dermatologic complication.
Insights
Pseudomyxoma retroperitonei from appendiceal cancer can cause a skin fistula. Gadolinium-enhanced MRI best shows pseudomyxoma features, aiding diagnosis of this rare abdominal condition.
Area of Science:
- Gastroenterology
- Oncology
- Radiology
Background:
- Pseudomyxoma retroperitonei is a rare condition characterized by mucinous ascites.
- It often originates from a mucinous neoplasm of the appendix.
Observation:
- A patient presented with pseudomyxoma retroperitonei originating from appendiceal mucinous carcinoma.
- The patient spontaneously developed a skin fistula, a rare complication.
Findings:
- Thick walls and septa, characteristic of pseudomyxoma, were clearly visualized.
- Gadolinium-enhanced magnetic resonance imaging (MRI) proved superior in demonstrating these features.
Implications:
- This case highlights the potential for pseudomyxoma to manifest as a cutaneous fistula.
- It suggests that intra-abdominal pseudomyxoma may initially present as a dermatologic issue, complicating diagnosis.