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Cystic fibrosis: nutritional consequences and management.
Bailliere'S Clinical Gastroenterology
|March 18, 1999
Summary
Maintaining adequate nutrition is crucial for cystic fibrosis (CF) patients, as malnutrition negatively impacts lung health and survival. Nutritional support should address underlying issues and prioritize simpler, cost-effective methods when possible.
Area of Science:
- Pulmonology
- Nutritional Science
- Gastroenterology
Background:
- Malnutrition is a significant negative prognostic factor in cystic fibrosis (CF).
- It adversely affects pulmonary disease progression and correlates inversely with survival rates.
- Achieving a positive energy balance is vital for maintaining nutritional status in CF patients.
Purpose of the Study:
- To review the importance of nutritional status in cystic fibrosis.
- To outline essential considerations before initiating nutritional supplementation.
- To evaluate various nutritional support strategies for CF patients.
Main Methods:
- Literature review of nutritional management in cystic fibrosis.
- Analysis of factors influencing nutritional status in CF.
- Comparison of different nutritional intervention methods.
Main Results:
- Pre-supplementation assessment must rule out conditions like pancreatic insufficiency and chronic infections.
- Various interventions exist, including oral nutrition, supplementation, enteral, and parenteral nutrition.
- Elemental nutrients offer no advantage over polymeric nutrients and are more costly.
Conclusions:
- Nutritional status is a critical determinant of outcomes in cystic fibrosis.
- Addressing underlying pathologies is a prerequisite for effective nutritional support.
- Simpler nutritional interventions, such as boosted oral intake or polymeric formulas, are preferred when goals are met.