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Double outlet right ventricle. Study of 27 cases
British Heart Journal
|November 1, 1976
Summary
This study examined 27 cases of double outlet right ventricle in children, identifying common associated defects like ventricular septal defect and pulmonary stenosis. Findings highlight specific conal abnormalities linked to great vessel stenosis and transposition.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Disease
- Cardiac Anatomy
Background:
- Double outlet right ventricle (DORV) is a complex congenital heart malformation.
- Understanding associated anomalies is crucial for diagnosis and management.
- Previous studies have varied in focus regarding associated defects.
Purpose of the Study:
- To anatomically characterize double outlet right ventricle (DORV).
- To identify and categorize common associated cardiac malformations in DORV.
- To correlate specific conal and great vessel abnormalities with DORV subtypes.
Main Methods:
- Anatomical examination of 27 pediatric hearts with DORV.
- Exclusion of cases with dextrocardia, situs inversus, or l-ventricular loop.
- Detailed analysis of the infundibular region, great vessels, and ventricular septum.
Main Results:
- Ventricular septal defect and pulmonary stenosis were the most frequent associated malformations.
- Aortic stenosis was predominant in neonatal deaths.
- Specific conal morphologies (aortic, pulmonary, double) were associated with distinct anomalies like VSD, pulmonary stenosis, and great vessel stenosis.
Conclusions:
- Double outlet right ventricle frequently coexists with other congenital heart defects, particularly VSD and pulmonary stenosis.
- Conal anatomy and great vessel status are important features in DORV.
- Detailed anatomical assessment is vital for understanding DORV and its variations.