[Sacro-coccygeal dysplasia and megarrectum in children (author's transl)]

35 cases of megarrectum associated with lumbo-sacro-coccygeal dysplasis are reviewed. 32.7% of the dysplasia were sacral. Nine cases were ultrashort aganglionic segments. Symptoms were variable, of early onset (82.7% before one year) and mild (57.1% required medical advise after three). Medical management was useful in the non aganglionic group whereas it was ineffective in the aganglionic group. Sphincteric myotomy was the more common operation used. Physiopathology and modalities of treatment are discussed.