[Acro-osteolysis idiopathic distal (author's transl)]

A six year old girl. With a clinical picture of acro-osteolysis idiopathic non familial associated with other anomalies is presented. Literature is reviewed and the clinical, radiologic, pathologic and etiopathogenetic features are commented, pointing out the diferent associated abnormalities that other authors did not consign: facial, anacraneal dysplasia, epiphyseal separations and dislocations of radius, and peroneal incurvation.