[Breast-like carcinoma of the vulva]

Breast-like carcinomas of the vulva is a rare finding. Only 11 cases are reported in the literature. This article reports a painful tumor of the left vulvar labia in a 62 year-old woman. Excisional biopsy showed an infiltrating adenocarcinoma, histologically similar to a breast tumor with positive hormonal receptors. The origin of this tumor, ectopic mammary tissue or specific adnexal genito-anal gland, is discussed. From data of the literature, we offer guidelines for diagnosis, treatment and origin of this rare tumor.