[Arrhythmogenic dysplasia of the right ventricle]

This paper is a case report of 58 years old patient with arrhytmogenic right ventricular dysplasia (ARVD), very rare cardiomyopathy of unknown cause who was in jeopardy because of recurrent ventricular tachycardia. ARVD is caused by abnormality in the development of the right ventricular musculature. In the right ventricular wall there are areas with a reduced number of myofibrils which are replaced by fatty and fibrous tissue. Therapy consists of drugs administration and DC cardioversion while surgical treatment is required in refractory cases.