Related Experiment Videos
Inflammatory pseudotumor of the liver in Kostmann's disease
1Department of Pediatric Hematology and Oncology, Chang Gung Children's Hospital, Kaohsiung, 123, Ta-Pei Road, Niao-Sung Hsiang, Kaohsiung, 833, Taiwan, Republic of China.
Pediatric Surgery International
|June 17, 1999
Abstract:
A case in which inflammatory pseudotumor of the liver (IPTL) seemed to complicate severe congenital neutropenia (Kostmann's disease) is reported. IPTL is a rare entity, especially in childhood. The exact etiology of this lesion is unknown, but it is generally regarded as a benign, reactive inflammatory condition. Based on 15 reported pediatric cases in the literature, the causes, diagnosis, and treatment of IPTL are discussed.