Fibrous lesion of the distal femur associated with angular deformity

Unilateral femoral angulation is uncommon. We describe two children with unilateral progressive distal femoral varus and limb-length discrepancy. These deformities were associated with a fibrous lesion involving the medial aspect of the distal femoral metaphysis. Both patients were 15 to 16 months old. In both, the deformity was progressive, resulting in excisional biopsy and osteotomy. The gross and microscopic appearance of both lesions was similar, and the histology was dense fibrous connective tissue. The patients' femoral alignment was maintained at follow-up of a minimum of 16-36 months. The etiology of these lesions is unknown; they are associated with progressive deformity and appear to respond well to surgical intervention.