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Unusual vascular dysplasia presenting as an intra-abdominal catastrophe
1Department of Paediatric Surgery, John Radcliffe Hospital, Headley Way, Headington, Oxford OX3 9DU.
Pediatric Surgery International
|July 23, 1999
Abstract:
A case of severe, generalised vascular dysplasia presenting as an intra-abdominal catastrophe is reported. Associated clinical features included cutis marmorata telangiectatica congenita, congenital glaucoma, hypertension, and focal fits. The case has been reported in view of its rarity and nature of presentation.