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An autopsy case of familial idiopathic dilatation of bilateral atria

M Arao1, S Shimizu, Y Miyatake

  • 1Department of Cardiology, Tokyo Metropolitan Komagome Hospital.

Internal Medicine (Tokyo, Japan)
|August 10, 1999
PubMed

Insights

This study reports a rare case of familial idiopathic dilatation of bilateral atria in a patient with congestive heart failure. The condition affected multiple family members, suggesting a genetic component.

Area of Science:

  • Cardiology
  • Genetics
  • Pathology

Background:

  • Congestive heart failure (CHF) management.
  • Idiopathic atrial dilatation as a rare condition.

Observation:

  • A 59-year-old male with CHF presented with remarkable bilateral atrial dilatation.
  • Normal coronary arteries, left ventricular contraction, and endomyocardial biopsy.
  • Dynamic magnetic resonance imaging (MRI) revealed similar atrial dilatation in siblings.

Findings:

  • Familial idiopathic dilatation of bilateral atria confirmed.
  • Proband experienced cardiogenic shock and mortality.
  • Pathology showed nonspecific changes in atria and ventricles.

Implications:

  • Highlights a rare genetic cardiac disorder.
  • Suggests the need for family screening in similar cases.
  • Contributes to understanding idiopathic atrial dilatation.

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