[Multifocal malignant transformation of extreme fibromatosis with pulmonary involvement]
B Hummel1, H J Schumann, B Hofmann
1Klinik für Innere Medizin, Städtisches Klinikum Dessau.
Pneumologie (Stuttgart, Germany)
|November 2, 1999
Abstract:
We report on the case of a 40-year old patient with extreme neurofibromatosis with severe kyphoskoliosis and deformation of the thorax. The patient died from malignant transformation which occurred multifocally with extensive pulmonary metastases. The well-known thoracic manifestations of neurofibromatosis are reviewed.
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