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[Primary pulmonary rhabdomyosarcoma: a case report]
J Badreddine1, J P Ledoux, E Marcade
1Cabinet d'anatomie et cytologie pathologiques Richier, rue J.-L. Bertrand, B.P. 7739, Atalante Villejean, 35077 Rennes Cedex.
Annales De Pathologie
|January 29, 2000
Abstract:
We report a case of primary pulmonary rhabdomyosarcoma in a 52-year-old woman. The diagnosis was established after radical right pneumonectomy, mainly based on immunohistochemistry and electron microscopy findings. This type of tumor is rare in adults. Its primary origin is suggested when a pulmonary meta-stasis of rhabdomyosarcoma from another site or a component of a mixed tumor are ruled out. The best treatment is surgery. The prognosis is poor.