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Kearns-Sayre syndromes an absolute indication for prophylactic implantation of definitive pacemaker?
H M Barragán-Campos1, C F Barrera-Ramírez, P Iturralde Torres
1Department of Internal Medicine, Instituto Nacional de la Nutrición Salvador Zubirán, México, D.F.
Abstract:
Kearns-Sayre syndrome is a mitochondrial cytopathy characterized by chronic progressive external ophthalmoplegia, retinitis pigmentosa and heart block, the last of which determines the survival of these patients. The case of a 23 year old man with Kearns-Sayre syndrome, conduction disturbances and mitral valve prolapse is presented. The characteristics of this syndrome are described and the criteria for prophylactic installation of a pacemaker discussed.