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Triple central ray amputation for clear cell sarcoma of the hand
1Baptist Medical Center and Hand Surgery Section/Orthopaedic Surgery Department, University of Oklahoma, Oklahoma City, USA.
American Journal of Orthopedics (Belle Mead, N.J.)
|April 4, 2000
Summary
Clear cell sarcoma, a rare soft tissue cancer, was diagnosed in a teenage girl. Limb salvage surgery involving triple finger amputation preserved hand function, highlighting the need for ongoing monitoring due to recurrence risks.
Area of Science:
- Orthopedic Oncology
- Surgical Oncology
- Pediatric Oncology
Background:
- Clear cell sarcoma (CCS) is a rare, aggressive soft tissue malignancy.
- Recurrent soft tissue masses require careful evaluation and management.
- Limb salvage surgery is an alternative to amputation for certain extremity tumors.
Observation:
- A 16-year-old female presented with a recurrent soft tissue mass on her left hand, diagnosed as clear cell sarcoma.
- The patient opted for limb salvage over amputation.
- A triple central ray amputation of the index, middle, and ring fingers was performed.
Findings:
- Three years post-surgery, the patient maintains reasonable grasp function with her remaining digits.
- She has elected not to use a prosthesis.
- Clear cell sarcoma has a high propensity for local recurrence and distant metastasis.
Implications:
- Limb salvage surgery can be a viable option for managing clear cell sarcoma of the hand, preserving functional outcomes.
- Long-term surveillance is crucial for patients with clear cell sarcoma due to frequent recurrence and metastatic potential.
- This case underscores the importance of multidisciplinary management for rare pediatric soft tissue sarcomas.