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Ebstein's anomaly with coarctation of the aorta. An unusual association

M Ebaid1, E Azeka, N M Ikari

  • 1Instituto do Coração do Hospital das Clínicas, FMUSP, Brazil.

Arquivos Brasileiros De Cardiologia
|February 7, 2001
PubMed

Insights

Ebstein's anomaly with coarctation of the aorta is rare. Surgical correction of coarctation showed good outcomes, but tricuspid valve dysplasia persisted in some patients.

Area of Science:

  • Cardiology
  • Pediatric Cardiology
  • Congenital Heart Disease

Background:

  • Ebstein's anomaly and coarctation of the aorta are rare co-occurring congenital heart defects.
  • This report details three male pediatric cases with this combined anomaly.

Observation:

  • Three male patients (7 months, 4 years, 14 years) presented with Ebstein's anomaly and coarctation of the aorta.
  • Two patients had atrioventricular and ventriculoarterial discordance, experiencing neonatal heart failure.
  • The third patient had concordance, Wolf-Parkinson-White syndrome, and paroxysmal tachycardia.

Findings:

  • All patients underwent successful surgical correction of coarctation of the aorta.
  • The patient with concordance received tricuspid valvuloplasty and anomalous pathway ablation.
  • Postoperative outcomes were good for two years, though tricuspid valve dysplasia persisted in discordant cases.

Implications:

  • Surgical correction of coarctation is feasible in complex Ebstein's anomaly.
  • Tricuspid valve dysplasia remains a challenge, requiring ongoing management.
  • This case series highlights the management of a rare congenital heart defect combination.

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