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Congenital Heart Surgery Nomenclature and Database Project: corrected (discordant) transposition of the great
J L Wilkinson1, A D Cochrane, T R Karl
1Department of Cardiology, Royal Children's Hospital, Melbourne, Australia.
Insights
This study clarifies nomenclature for congenitally corrected transposition of the great arteries (ccTGA). A unified reporting system and database are proposed to improve risk stratification and data sharing for this complex congenital heart defect.
Area of Science:
- Cardiology
- Congenital Heart Surgery
- Medical Informatics
Background:
- Congenitally corrected transposition of the great arteries (ccTGA) presents complex cardiac anatomy.
- Existing nomenclature for ccTGA is variable and confusing, hindering consistent reporting.
- ccTGA is often associated with ventricular septal defects, outflow tract obstruction, and tricuspid valve abnormalities.
Purpose of the Study:
- To establish a unified nomenclature and reporting system for ccTGA.
- To clarify synonymous and nonsynonymous appellations for ccTGA.
- To lay the foundation for comprehensive risk stratification analyses in ccTGA.
Main Methods:
- Review and debate of existing ccTGA nomenclature by experts from the STS-Congenital Heart Surgery Database Committee and EACTS.
- Development of a hierarchical database scheme for ccTGA data entry.
- Presentation of a minimum database set for data sharing and trend interpretation.
Main Results:
- A clarified terminology for ccTGA is presented, identifying synonymous terms.
- A comprehensive and a minimum database set for ccTGA are proposed.
- Outcome tables correlating diagnoses, procedures, and risk factors are provided.
Conclusions:
- A unified nomenclature and database system are essential for consistent reporting of ccTGA.
- The proposed system facilitates data sharing and supports risk stratification for ccTGA patients.
- Standardized reporting will improve the understanding and management of this complex congenital heart defect.
Abstract:
The extant nomenclature for congenitally corrected transposition of the great arteries is reviewed for the purpose of establishing a unified reporting system. The subject was debated and reviewed by members of the STS-Congenital Heart Surgery Database Committee and representatives from the European Association for Cardiothoracic Surgery. All efforts were made to include all relevant nomenclature categories using synonyms where appropriate. Congenitally corrected transposition of the great arteries is a complex cardiac lesion that is associated with ventricular septal defect, left ventricular outflow tract obstruction, and tricuspid valve abnormalities. Nomenclature for this lesion has been variable and confusing. Herein we attempt to clarify the terminology, with an emphasis on identification of synonymous and nonsynonymous appellations. A comprehensive database set is presented that is based on a hierarchical scheme. Data are entered at various levels of complexity and detail that can be determined by the clinician. These data can lay the foundation for comprehensive risk stratification analyses. A minimum database set is also presented that will allow for data sharing and would lend itself to basic interpretation of trends. Outcome tables relating diagnoses, procedures, and various risk factors are presented.
