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Deliberate sulphonylurea poisoning mimicking hyperinsulinaemia of infancy

L Owen1, M Ellis, J Shield

  • 1Bristol Children's Hospital, Bristol, UK.

Insights

A six-month-old infant experienced seizures due to hyperinsulinism and hypoglycemia. High blood sulfonylurea levels suggested intentional ingestion, pointing to Munchausen syndrome by proxy as a critical consideration in infant hypoglycemia cases.

Area of Science:

  • Pediatrics
  • Endocrinology
  • Toxicology

Background:

  • Infantile hypoglycemia is a critical condition requiring prompt diagnosis.
  • Hyperinsulinism is a common cause of persistent hypoglycemia in infants.
  • Munchausen syndrome by proxy (MSbP) is a rare but serious form of child abuse.

Observation:

  • A 6-month-old infant presented with seizures and documented hypoglycemia.
  • Family history revealed type II diabetes.
  • Elevated blood sulfonylurea levels were detected in the infant.

Findings:

  • The infant's hypoglycemia was secondary to hyperinsulinism.
  • The high sulfonylurea levels indicated exogenous ingestion.
  • A multidisciplinary team diagnosed probable Munchausen syndrome by proxy.

Implications:

  • MSbP should be considered in the differential diagnosis of unexplained infantile hypoglycemia.
  • Early recognition and intervention are crucial for the child's well-being.
  • This case highlights the importance of considering non-medical causes of severe infant illness.

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