Hemitricuspid dysplasia in association with ventricular septal defect

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S Victor1, V M Nayak

  • 1The Heart Institute, Chennai, India.

Texas Heart Institute Journal
|June 1, 2000
PubMed

Insights

Tricuspid valve leaflet dysplasia, associated with perimembranous ventricular septal defects, affects specific septal regions. Surgical findings highlight this complex congenital heart anomaly.

Area of Science:

  • Cardiovascular Surgery
  • Congenital Heart Disease
  • Cardiac Anatomy

Background:

  • The tricuspid valve comprises septal, anterior, and posterior leaflets with distinct chordopapillary support.
  • Tricuspid valve support is anatomically divided into two main groups based on septal and mural leaflet relationships.
  • Understanding this anatomical division is crucial for diagnosing and managing tricuspid valve abnormalities.

Observation:

  • A specific group of chordopapillary support is linked to the bulbar, perimembranous, and sinus regions of the interventricular septum.
  • Another support group connects to the trabecular septum and adjacent free wall.

Findings:

  • This study reports surgical findings in 5 patients with tricuspid valve leaflet dysplasia.
  • The observed dysplasia involved leaflets and chordopapillary support related to the bulbar, perimembranous, and sinus interventricular septum.
  • All patients also presented with a perimembranous ventricular septal defect.

Implications:

  • The findings suggest a significant association between specific tricuspid valve anomalies and perimembranous ventricular septal defects.
  • Discusses phylogenic, ontogenic, and surgical implications of this cardiac anomaly.
  • Highlights the importance of detailed anatomical assessment in complex congenital heart disease.

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