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[Cystic fibrosis in the Western health region]

G Fluge1

  • 1Barneklinikken Haukeland Sykehus, Bergen.

Tidsskrift for Den Norske Laegeforening : Tidsskrift for Praktisk Medicin, Ny Raekke
|June 2, 2000
PubMed

Insights

Cystic fibrosis survival rates in Western Norway have significantly improved, with patients born after 1990 all being alive. This indicates a positive outlook for cystic fibrosis patient longevity in the region.

Area of Science:

  • Medical Research
  • Pulmonology
  • Genetics

Context:

  • Cystic fibrosis (CF) is a genetic disorder affecting multiple organs.
  • Western Norway has a diagnosed population of 78 CF patients since 1960.
  • Geographic distribution shows Hordaland county as the most affected region.

Purpose:

  • To analyze survival trends and demographic data of cystic fibrosis patients in Western Norway.
  • To compare regional CF patient outcomes with national and international data.
  • To assess the impact of improved medical care on CF patient longevity.

Summary:

  • Survival rates for cystic fibrosis patients in Western Norway have shown marked improvement, particularly for those diagnosed after 1990.
  • The cohort born before 1971 had a 71% survival rate, increasing to 91% for those born between 1971-1990.
  • Pseudomonas aeruginosa infection rates are lower than the Norwegian average, potentially contributing to better outcomes.

Impact:

  • Western Norway's CF patient survival rates are favorable compared to international benchmarks.
  • The study suggests a realistic expectation for median survival to exceed 30 years for current CF patients.
  • Findings highlight the effectiveness of regional healthcare strategies for cystic fibrosis management.

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