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Ear, nose and throat findings in cystic fibrosis patients

T Ozçelik1, N Ozgirgin, U Ozçelik

  • 1Department of Otolaryngology, Bayindir Medical Center, Hacettepe University Faculty of Medicine, Ankara.

The Turkish Journal of Pediatrics
|January 1, 1997
PubMed

Insights

Children with cystic fibrosis (CF) have a higher risk of ear-nose-throat diseases like sinusitis and nasal polyps. However, significant hearing problems are uncommon in these patients.

Area of Science:

  • Otolaryngology
  • Pediatrics
  • Genetics

Background:

  • Cystic Fibrosis (CF) is a genetic disorder affecting multiple organs.
  • Ear-nose-throat (ENT) complications are frequently observed in CF patients.
  • Understanding the prevalence of specific ENT conditions in pediatric CF is crucial for timely diagnosis and management.

Purpose of the Study:

  • To investigate the prevalence and types of ear-nose-throat diseases in children with cystic fibrosis.
  • To assess the association between cystic fibrosis and common ENT conditions.
  • To determine the audiological status in this pediatric cohort.

Main Methods:

  • A cross-sectional survey was conducted on 30 pediatric patients diagnosed with cystic fibrosis.
  • Patients ranged in age from 2 to 17 years.
  • Standard otolaryngological examinations and audiological assessments were performed.

Main Results:

  • 10% of patients had secretory otitis media.
  • Chronic pansinusitis was present in 33% of cases, with mild response to medical therapy.
  • Nasal conchae hypertrophy was observed in 27% of children, and one had prior polyp surgery.
  • Hearing impairment was not a common finding.

Conclusions:

  • Pediatric patients with cystic fibrosis exhibit an increased risk for certain ENT conditions, including sinusitis and nasal polyps.
  • While ENT diseases are more prevalent, significant audiological issues are less common.
  • Nasal polyps, hypertrophied turbinates, or refractory sinusitis in children warrant consideration for cystic fibrosis.

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