Related Experiment Video
Updated: Aug 7, 2026
Performing Intracochlear Electrocochleography During Cochlear Implantation
Published on: March 8, 2022
Cochlear implantation in auditory neuropathy
R T Miyamoto1, K I Kirk, J Renshaw
1Department of Otolaryngology--Head and Neck Surgery, Indiana University School of Medicine, Indianapolis 46202, USA.
Objective:
Auditory neuropathy is a recently described clinical entity characterized by sensorineural hearing loss in which the auditory evoked potential (ABR) is absent but otoacoustic emissions are present. This suggests a central locus for the associated hearing loss. In this study the results observed in a child with auditory neuropathy who received a cochlear implant are presented and compared with those of a matched group of children who were recipients of implants.
Methods:
A single-subject, repeated-measures design, evaluating closed-set and open-set word recognition abilities was used to assess the subject and a control group of matched children with implants who had also experienced a progressive sensorineural hearing loss.
Results:
The subject demonstrated improvements in vowel recognition (82% correct) by 1 year after implantation, which were only slightly lower than the control group. Consonant recognition and open-set word recognition scores were significantly lower.
Conclusion:
Caution should be exercised when considering cochlear implantation in children with auditory neuropathy. As with conventional hearing aids, less than optimal results may be seen.
