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Published on: October 12, 2012
Paediatric Behçet disease manifested as recurrent myositis: from an incomplete to a full-blown form
Y Uziel1, A Lazarov, M Cordoba
1Department of Paediatrics, Sapir Medical Centre, Tel Aviv University Sackler School of Medicine, Kfar-Saba, Israel. Uziely@inter.net.il
Insights
Recurrent myositis, a rare symptom of Behçet disease, can manifest in children. Early diagnosis of this autoimmune condition is crucial for effective management and preventing severe outcomes.
Area of Science:
- Rheumatology
- Pediatrics
- Neurology
Background:
- Behçet disease is a rare multisystemic inflammatory disorder.
- Myositis, or muscle inflammation, is an uncommon manifestation of Behçet disease, particularly in pediatric cases.
- Early diagnosis of Behçet disease in children is often challenging due to incomplete symptom presentation.
Observation:
- A 12-year-old boy presented with recurrent episodes of localized calf myositis.
- The myositis episodes were responsive to corticosteroid treatment.
- A diagnosis of Behçet disease was established after a 3-year follow-up period.
Findings:
- This case highlights recurrent localized myositis as a primary manifestation of Behçet disease in a pediatric patient.
- The study underscores the potential for incomplete Behçet disease to evolve into a more severe form, emphasizing muscle involvement.
- The findings suggest that myositis should be considered in the differential diagnosis of unexplained calf pain and limping in children.
Implications:
- Early recognition of myositis in children may lead to earlier diagnosis of Behçet disease.
- Prompt diagnosis and management of Behçet disease can prevent long-term complications.
- This case emphasizes the importance of considering rare presentations of Behçet disease in pediatric rheumatology and neurology.
Unlabelled:
A 12-year-old boy presented with a limp and findings suggesting localised myositis of his right calf and a working diagnosis of Behçet disease was made. During 3 years of follow-up, he had another three episodes of calf myositis, all responsive to corticosteroids within days.
Conclusion:
A case of recurrent localised myositis as a main manifestation of Behçet disease is reported. The evolution of incomplete Behçet disease, which is common in children, to the full blown form, with the emphasis on muscle involvement and the importance of early diagnosis of Behçet disease, is discussed.
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