Mitochondrial import of mammalian branched-chain alpha-keto acid dehydrogenase complex subunits

Controlled overexpression of BCKD kinase expression: metabolic engineering applied to BCAA metabolism in a mammalian system.

Metabolic engineering·2000

Gene preference in maple syrup urine disease.

American journal of human genetics·2000

Amino acid deprivation induces translation of branched-chain alpha-ketoacid dehydrogenase kinase.

American journal of physiology. Cell physiology·2000

Import rate of the E1beta subunit of human branched chain alpha-ketoacid dehydrogenase is a limiting factor in the amount of complex formed in the mitochondria.

Biochimica et biophysica acta·1998

Murine branched chain alpha-ketoacid dehydrogenase kinase; cDNA cloning, tissue distribution, and temporal expression during embryonic development.

Gene·1998

Human mutations affecting branched chain alpha-ketoacid dehydrogenase.

Frontiers in bioscience : a journal and virtual library·1998

Comparative methods for recombinant production and characterization of 1-deoxy-D-xylulose-5-phosphate synthase from bacterial and apicomplexan sources.

Methods in enzymology·2026

Current methods and applications in the study of 1-Deoxy-D-xylulose 5-phosphate synthase (DXPS).

Methods in enzymology·2026

Thiamine pyrophosphate-dependent enzymes in Toxoplasma gondii and functional significance of an apicoplast-localized pyruvate dehydrogenase.

Methods in enzymology·2026

Biochemical and cryo-EM studies of the pyruvate dehydrogenase complex from native cell extracts.

Methods in enzymology·2026

Synthesis of phosphonate and phosphinate analogs of 2-oxo acids for site-specific inhibition of thiamine-diphosphate-dependent dehydrogenases of 2-oxo acids in vivo.

Methods in enzymology·2026

Use of dihydroxyacetone synthase for the assimilation of methanol in E. coli.

Methods in enzymology·2026

INDIVIDUAL ARTICLE: Ammonium Lactate in Clinical Practice: Optimizing Treatment of Xerotic and Hyperkeratotic Skin Conditions.

Journal of drugs in dermatology : JDD·2026

Modern Diagnosis and Management of Acid-Related Disorders.

Clinical gastroenterology and hepatology : the official clinical practice journal of the American Gastroenterological Association·2026

PABMB: connecting molecular biosciences across the Americas.

Trends in biochemical sciences·2026

Automated machine learning-Assisted interpretation of GC-MS urinary organic acid profiles by integrating explicit metabolic markers and chromatographic patterns for rare organic acidemias.

Talanta·2026

Diffuse Serous Atrophy of Bone Marrow in the Ankle and Hindfoot with Focal Acute Lateral Malleolar Osteomyelitis: A Magnetic Resonance Imaging-Based Case Report.

Foot & ankle specialist·2026

Effects of sex, treatment resistance, and antidepressant treatment on monoamine oxidase B total distribution volume.

medRxiv : the preprint server for health sciences·2026

Related Experiment Videos

Mitochondrial import of mammalian branched-chain alpha-keto acid dehydrogenase complex subunits

Related Concept Videos

Controlled overexpression of BCKD kinase expression: metabolic engineering applied to BCAA metabolism in a mammalian system.

Gene preference in maple syrup urine disease.

Amino acid deprivation induces translation of branched-chain alpha-ketoacid dehydrogenase kinase.

Import rate of the E1beta subunit of human branched chain alpha-ketoacid dehydrogenase is a limiting factor in the amount of complex formed in the mitochondria.

Murine branched chain alpha-ketoacid dehydrogenase kinase; cDNA cloning, tissue distribution, and temporal expression during embryonic development.

Human mutations affecting branched chain alpha-ketoacid dehydrogenase.

Comparative methods for recombinant production and characterization of 1-deoxy-D-xylulose-5-phosphate synthase from bacterial and apicomplexan sources.

Current methods and applications in the study of 1-Deoxy-D-xylulose 5-phosphate synthase (DXPS).

Thiamine pyrophosphate-dependent enzymes in Toxoplasma gondii and functional significance of an apicoplast-localized pyruvate dehydrogenase.

Biochemical and cryo-EM studies of the pyruvate dehydrogenase complex from native cell extracts.

Synthesis of phosphonate and phosphinate analogs of 2-oxo acids for site-specific inhibition of thiamine-diphosphate-dependent dehydrogenases of 2-oxo acids in vivo.

Use of dihydroxyacetone synthase for the assimilation of methanol in E. coli.

INDIVIDUAL ARTICLE: Ammonium Lactate in Clinical Practice: Optimizing Treatment of Xerotic and Hyperkeratotic Skin Conditions.

Modern Diagnosis and Management of Acid-Related Disorders.

PABMB: connecting molecular biosciences across the Americas.

Automated machine learning-Assisted interpretation of GC-MS urinary organic acid profiles by integrating explicit metabolic markers and chromatographic patterns for rare organic acidemias.

Diffuse Serous Atrophy of Bone Marrow in the Ankle and Hindfoot with Focal Acute Lateral Malleolar Osteomyelitis: A Magnetic Resonance Imaging-Based Case Report.

Effects of sex, treatment resistance, and antidepressant treatment on monoamine oxidase B total distribution volume.

Related Experiment Videos

Mitochondrial import of mammalian branched-chain alpha-keto acid dehydrogenase complex subunits

Related Concept Videos

Related Articles