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Cardiac involvement in total generalized lipodystrophy (Berardinelli- Seip syndrome)
R F Viégas1, R V Diniz, T M Viégas
1Escola Paulista de Medicina, Universidade Federal de São Paulo, São Paulo, SP, Brazil.
Arquivos Brasileiros De Cardiologia
|October 6, 2000
Abstract:
Total generalized lipodystrophy (Berardinelli - Seip Syndrome) is a rare hereditary disease characterized by insulin-resistant diabetes mellitus and a small quantity of adipose tissue and is of unknown origin. Common cardiovascular alterations related to this syndrome are cardiac hypertrophy and arterial hypertension. This article reports a case of Berardinelli - Seip syndrome and reviews the literature with special emphasis on the cardiovascular manifestations of this syndrome.