VIPoma of pancreas in a child

S C Samal1, A C Paul, S Venkateswari

  • 1Department of Gastrointestinal Sciences, Christian Medical College and Hospital, Vellore. subashsamal@hotmail.com

Insights

A young girl

Area of Science:

  • Pediatric Endocrinology
  • Surgical Oncology

Background:

  • VIPoma is a rare neuroendocrine tumor.
  • It often presents with secretory diarrhea.

Observation:

  • An eleven-year-old female presented with massive watery diarrhea.
  • Diagnostic workup revealed a pancreatic VIPoma.

Findings:

  • Surgical resection of the pancreatic VIPoma led to a favorable clinical response.
  • No tumor recurrence was observed at 18 months post-surgery.

Implications:

  • Surgical management is effective for pediatric pancreatic VIPoma.
  • Complete tumor resection offers a good prognosis with long-term disease-free survival.

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