Related Experiment Video
Updated: Aug 4, 2026

Echocardiographic Evaluation of Atrial Communications before Transcatheter Closure
Published on: February 8, 2022
Tricuspid Atresia
Rao1
1Division of Pediatric Cardiology, Saint Louis University School of Medicine, 1465 South Grand Boulevard, St. Louis, MO 63104, USA. raops@slu.edu
Insights
Tricuspid atresia (TA) treatment has improved significantly with the Fontan principle. Staged total cavopulmonary connection is the preferred surgical approach for children with TA, offering a better outlook.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Disease Surgery
- Cardiovascular Physiology
Background:
- Tricuspid atresia (TA) historically has a poor prognosis.
- Advances in surgical techniques, including the Fontan principle, have improved outcomes for children with TA.
- Prompt palliative procedures are crucial for managing pulmonary blood flow and obstructions in TA.
Purpose of the Study:
- To review the current surgical management of tricuspid atresia (TA).
- To highlight the efficacy of staged total cavopulmonary connection in improving long-term outlook for TA patients.
- To compare the outcomes of total cavopulmonary diversion with conventional Fontan-Kreutzer operations.
Main Methods:
- Review of palliative procedures for tricuspid atresia.
- Description of staged total cavopulmonary connection, including bidirectional Glenn procedure and extracardiac conduit diversion.
- Comparison of total cavopulmonary diversion with conventional Fontan-Kreutzer operations.
Main Results:
- Staged total cavopulmonary connection is the current procedure of choice for surgical management of TA.
- This approach bypasses the right atrium and right ventricle.
- Total cavopulmonary diversion shows potential superiority over conventional Fontan-Kreutzer operations.
Conclusions:
- The long-term outlook for children with tricuspid atresia has markedly improved with modern surgical therapies.
- Staged total cavopulmonary connection represents a significant advancement in TA management.
- Further long-term follow-up studies are necessary to definitively confirm the superiority of total cavopulmonary diversion.
Abstract:
Untreated, the prognosis for patients with tricuspid atresia (TA) is poor. Recent advances in medical and surgical therapy, particularly the application of Fontan principle, have markedly improved the long-term outlook for children with this condition. Palliative procedures to normalize the pulmonary blood flow and to relieve interatrial or interventricular obstruction should be undertaken promptly. Staged total cavopulmonary connection to bypass the right atrium and right ventricle by an initial bidirectional Glenn procedure and followed by extracardiac conduit diversion of inferior vena caval flow into the pulmonary arteries appears to be the current procedure of choice in the surgical management of TA. Total cavopulmonary diversion appears to be superior to conventional Fontan-Kreutzer operations, but long-term follow-up results are needed to confirm this impression.
Related Concept Videos
Chambers of the Heart
Deoxygenated blood from the body is received in the right...
Heart Valves
The AV valves prevent the backflow of blood from the ventricles to the atria during ventricular contraction. These valves function with the assistance of the chordae tendineae and papillary muscles. When the ventricles are relaxed, the chordae tendineae are slack, allowing blood to flow from the atria into the...
Fetal Circulation
Two umbilical arteries transport blood from the fetus to the placenta. At the placenta, the blood absorbs oxygen and nutrients while simultaneously eliminating waste products. This oxygen-enriched and nutrient-rich blood then returns to the fetus through one...
Cardiovascular System Abnormal Findings II: Auscultation
Abnormal Heart Sounds
Gallops:
Mitral Stenosis I: Introduction
Mitral Stenosis II: Clinical features and Diagnostic Tests

