Intracranial venous anomalies associated with atretic cephalocoeles

F Brunelle1, J Baraton, D Renier

  • 1Department of Paediatric Radiology, Hôpital Necker-Enfants Malades, Paris, France. Brunelle@necker.fr

Pediatric Radiology
|December 2, 2000
PubMed

Insights

Intracranial venous anomalies are common in children with atretic cephalocoeles, particularly those located superiorly. These anomalies, including sinus abnormalities, are part of the broader dysraphic state.

Area of Science:

  • Pediatric Neurosurgery
  • Neuroradiology
  • Developmental Neuroscience

Background:

  • Midline scalp lesions, including soft-tissue masses and atretic cephalocoeles, are common in children.
  • Accurate diagnosis is crucial as treatment varies.
  • Intracranial venous anomalies are a known association with atretic cephalocoeles.

Purpose of the Study:

  • To determine the frequency of intracranial venous anomalies in children with atretic meningocoeles.
  • To characterize the types of venous anomalies associated with these lesions.

Main Methods:

  • Retrospective study of 31 pediatric patients with atretic cephalocoeles.
  • Magnetic Resonance Imaging (MRI) was used for assessment.
  • Analysis included 13 meningocoeles and 14 encephalocoeles.

Main Results:

  • Intracranial venous anomalies were identified in cephalocoeles located above the torcular.
  • Observed anomalies included absence of the straight sinus and duplication of the superior longitudinal sinus.

Conclusions:

  • Intracranial venous anomalies are frequently observed in atretic cephalocoeles.
  • These anomalies are considered an integral component of the underlying dysraphic state.
Abstract

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