Congenital cystic adenomatoid malformation in an adult presenting as lung abscess

J Dahabreh1, C Zisis, M Vassiliou

  • 1Thoracic Surgery Department, Saint Savas Anticancer Hospital, Athens, Greece. dkakats@cc.uoa.gr

Insights

Congenital cystic adenomatoid malformation (CCAM) in a 21-year-old male presented with recurrent lung infections. Surgical removal (right lower lobectomy) addressed a large mass, discussing the tumor's characteristics and prognosis.

Area of Science:

  • Pediatric Surgery
  • Thoracic Oncology
  • Pulmonology

Background:

  • Congenital cystic adenomatoid malformation (CCAM) is a rare congenital lung malformation.
  • Early-onset recurrent pulmonary infections can indicate underlying congenital lung disease.

Observation:

  • A 21-year-old male presented with a history of recurrent infant pulmonary infections.
  • A significant mass infiltrating the right lower lobe was identified, suspected as a lung abscess.

Findings:

  • Right lower lobectomy was performed to resect the mass.
  • The case facilitates discussion on CCAM's clinical features, diagnostics, pathology, and treatment.

Implications:

  • This case highlights the importance of considering CCAM in infants with recurrent respiratory issues.
  • Understanding CCAM's etiopathology and prognosis is crucial for effective patient management.

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