Jove
Visualize
Contact Us
JoVE
x logofacebook logolinkedin logoyoutube logo
ABOUT JoVE
OverviewLeadershipBlogJoVE Help Center
AUTHORS
Publishing ProcessEditorial BoardScope & PoliciesPeer ReviewFAQSubmit
LIBRARIANS
TestimonialsSubscriptionsAccessResourcesLibrary Advisory BoardFAQ
RESEARCH
JoVE JournalMethods CollectionsJoVE Encyclopedia of ExperimentsArchive
EDUCATION
JoVE CoreJoVE BusinessJoVE Science EducationJoVE Lab ManualFaculty Resource CenterFaculty Site
Terms & Conditions of Use
Privacy Policy
Policies

Related Experiment Videos

[Auditory neuropathies in infants].

A Morant Ventura1, M Orts Alborch, J García Callejo

  • 1Servicio de ORL, Hospital Clínico de Valencia, Universidad de Valencia.

Acta Otorrinolaringologica Espanola
|January 6, 2001
PubMed
Summary
This summary is machine-generated.

Related Concept Videos

You might also read

Related Articles

Articles linked to this work by shared authors, journal, and citation graph.

Sort by
Same author

Clinical Outcomes of Soft Tissue Preservation Surgery With Hydroxyapatite-Coated Abutments Compared to Traditional Percutaneous Bone Conduction Hearing Implant Surgery-A Pragmatic Multi-Center Randomized Controlled Trial.

Frontiers in surgery·2020
Same author

[Nasal packing in posterior epistaxis. Comparison of two methods].

Acta otorrinolaringologica espanola·2010
Same author

[Petrous bone fracture. Our experience: 1999-2004].

Acta otorrinolaringologica espanola·2007
Same author

[Management of peritonsillar infections].

Anales de pediatria (Barcelona, Spain : 2003)·2006
Same author

[Correlation between the contralateral supressor effect and the auditory fatigue using transitory acoustic otoemissions].

Acta otorrinolaringologica espanola·2006
Same author

[Immunomediation or hyperviscosity in rapidly progressive sensorineural hearing loss. A therapeutic approach].

Acta otorrinolaringologica espanola·2006
Same journal

Transoral Laser Microsurgery for Early Glottic Carcinoma: Laryngeal Preservation and Long-term Oncological Outcomes in 161 Patients.

Acta otorrinolaringologica espanola·2026
Same journal

A Case of Langerhans Cell Histiocytosis Masquerading as Benign Pediatric Head and Neck Lesions: A Diagnostic Pitfall.

Acta otorrinolaringologica espanola·2026
Same journal

Cochlear Implantation in a Child with Biallelic RDX Variant (DFNB24): Long-Term Auditory Outcome.

Acta otorrinolaringologica espanola·2026
Same journal

Hearing in Sickle Cell Disease: Cochlear and Subcortical Dysfunction without Cortical Impairment.

Acta otorrinolaringologica espanola·2026
Same journal

Effects of Systemic Clonidine Administration on Blood Loss and Surgical Field Quality in Functional Endoscopic Sinus Surgery.

Acta otorrinolaringologica espanola·2026
Same journal

Spanish validation of the Dyspnea Index (DI): translation, cultural adaptation, and psychometric evaluation.

Acta otorrinolaringologica espanola·2026
See all related articles

Auditory neuropathy presents differently in infants, impacting hearing development. Early diagnosis and tailored management are crucial for optimal outcomes in children with this auditory disorder.

Area of Science:

  • Audiology
  • Pediatric Neurology
  • Genetics

Background:

  • Auditory neuropathy spectrum disorder (ANSD) is a complex hearing impairment affecting auditory nerve function.
  • It is characterized by abnormal auditory evoked potentials (AEPs) with intact cochlear outer hair cell function.
  • The pathophysiology of ANSD is diverse, leading to varied impacts on hearing.

Observation:

  • Two infant cases of ANSD are presented, highlighting diagnostic and management differences.
  • Case 1: An infant girl with no risk factors showed absent AEPs despite present otoacoustic emissions, progressing to profound sensorineural hearing loss.
  • Case 2: An infant boy screened for hyperbilirubinemia exhibited ANSD, with destructured AEPs but evidence of residual hearing, indicating moderate hearing loss.

Findings:

Related Experiment Videos

  • Infants with auditory neuropathy can present with varying degrees of hearing loss, from profound to moderate.
  • Diagnostic evaluations including otoacoustic emissions and auditory evoked potentials are key in identifying ANSD.
  • The progression and residual hearing capacity in ANSD cases can differ significantly.

Implications:

  • This study underscores the importance of early and accurate diagnosis of auditory neuropathy in infants.
  • Tailored audiological management strategies are essential for infants diagnosed with ANSD.
  • Further research into the diverse etiologies and prognoses of ANSD is warranted for improved clinical practice.