[Left to right shunt for congenital coronary arterio-venous fistulas]

P Baello1, B Sevilla, I Roldán

  • 1Servicio de Cardiología. Hospital Universitario Dr. Peset. Valencia.

Insights

Congenital coronary artery fistulas are rare heart defects. This case highlights three fistulas in an asymptomatic child, detected via heart murmur.

Area of Science:

  • Cardiology
  • Pediatric Cardiology
  • Congenital Heart Disease

Background:

  • Congenital coronary artery fistulas (CCAFs) are uncommon cardiac malformations.
  • CCAFs can lead to serious complications like heart failure and pulmonary hypertension.
  • Spontaneous closure of CCAFs can occur, but monitoring is crucial.

Observation:

  • A 10-year-old asymptomatic male presented with an incidental heart murmur.
  • Diagnostic imaging revealed three distinct coronary artery fistulas.
  • Two fistulas originated from the left coronary artery, draining into the right ventricle.
  • One fistula originated from the right coronary artery, draining into the pulmonary artery trunk.

Findings:

  • The patient was asymptomatic despite the presence of multiple coronary artery fistulas.
  • Doppler echocardiography and angiography confirmed the diagnosis and anatomical details.
  • The specific drainage patterns into the right ventricle and pulmonary artery were identified.

Implications:

  • Early detection of CCAFs, even in asymptomatic individuals, is vital.
  • Understanding fistula anatomy aids in surgical or interventional planning.
  • This case underscores the importance of echocardiography and angiography in diagnosing CCAFs.

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