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Postoperative coma in a child with carnitine palmitoyltransferase I deficiency
P T Neuvonen1, A A van den Berg
1Department of Anesthesia, King Fahd Armed Forces Hospital, Jeddah, Saudi Arabia. pekka_neu@hotmail.com
Anesthesia and Analgesia
|February 28, 2001
Abstract
Implications:
We describe prolonged drowsiness proceeding to hepatic encephalopathy in a child with sickle cell trait and carnitine palmitoyltransferase deficiency. The latter defect of fatty acid metabolism is associated with striated muscle dysfunction and hepatic failure.