Related Experiment Videos
Occipital meningocele and Mondini deformity of the cochlea
O D Smith1, A M Neumann, K S Sirimanna
1Departments of Audiology and ENT Surgery, Great Ormond Street Hospital for Sick Children, London, UK.
The Journal of Laryngology and Otology
|March 10, 2001
Abstract:
We present two cases of a previously unreported association between occipital meningocele and Mondini deformity of the cochlea. The probability of the association is supported by the intimate relationship between the development of these structures; the existence of dysembryoplastic factors that can cause both abnormalities; and the universal existence of cochlear abnormalities in anencephalic foetuses. The importance of considering the association is emphasized, in terms of early identification and referral of children with hearing loss, and avoidance of duplication of investigations.