Amyloidosis of the tongue with kappa light chain disease
P Y Basak1, S Ergin, M T Sezer
1Department of Dermatology, Faculty of Medicine, Suleyman Demirel University, Isparta, Turkey.
The Australasian Journal of Dermatology
|March 10, 2001
Abstract:
A 70-year-old woman presented with a painful, red tongue with papules associated with xerostomia and systemic symptoms including weight loss, difficulty in swallowing and breathing, haemochezia and leg swelling. Biopsy from the tongue demonstrated amyloid deposits and, on further investigation, kappa chain disease was diagnosed. Primary systemic amyloidosis was diagnosed and the patient died within weeks of presentation.
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