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Constitutively activating mutation in WASP causes X-linked severe congenital neutropenia

K Devriendt1, A S Kim, G Mathijs

  • 1Centre for Human Genetics, University Hospital Leuven, Leuven, Belgium.

Nature Genetics
|March 10, 2001
PubMed
Summary

A new disease, X-linked severe congenital neutropenia (XLN), is caused by a mutation in the Wiskott-Aldrich syndrome protein (WASP) gene. This mutation leads to constitutive activation of WASP, disrupting actin cytoskeleton regulation in hematopoietic cells.

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