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Updated: Oct 9, 2026

Cox-Maze IV Procedure Concomitant with Valvular Surgery In Situs Inversus Dextrocardia: A Single-Center Experience in China
Published on: February 11, 2022
[Atrioventricular discordance. Clinico-surgical experience 1990-2000]
1Servicio de Cardiopatías Congénitas, Hospital de Cardiología, CMN Siglo XXI. Avenida Cuauhtémoc 330, Col. Doctores, México, D.F. alva1@prodigy.com.mx
Insights
This study analyzed atrioventricular discordance, finding common associated lesions like ventricular septal defects. Surgical outcomes show high mortality and pacemaker needs for atrioventricular block.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Disease
- Cardiac Surgery
Background:
- Atrioventricular discordance is a complex congenital heart defect.
- Understanding its variations and outcomes is crucial for surgical planning.
Purpose of the Study:
- To determine the incidence of ventriculoarterial connections with atrioventricular discordance.
- To identify associated cardiac lesions.
- To evaluate surgical results, including mortality and complications.
Main Methods:
- Retrospective analysis of patients diagnosed with atrioventricular discordance via echocardiography between 1990 and March 2000.
- Detailed review of patient demographics, cardiac anatomy, associated lesions, and surgical interventions.
Main Results:
- Thirty-six patients with atrioventricular discordance were identified, with ages ranging from infancy to adulthood.
- The most frequent ventriculoarterial connection was discordant (77.7%). Ventricular septal defects with pulmonary stenosis or atresia were common associated lesions (58%).
- Surgical interventions included palliative and corrective procedures, with one anatomical correction. High operative mortality (40.1%) and significant rates of postoperative atrioventricular block requiring pacemakers (40.1%) were observed.
Conclusions:
- Right ventricular dysfunction is a notable complication in patients with atrioventricular discordance.
- Surgical management of atrioventricular discordance is associated with high mortality and a substantial need for pacemakers due to atrioventricular block.
Objective:
To know the incidence of ventriculoarterial connections combined with atrioventricular discordance, associated lesions and surgical results, including the first case with anatomical correction.
Method:
All patients with atrioventricular discordance by echocardiography from 1990 to March 2000 were analyzed.
Results:
Thirty six patients with atrioventricular discordance were found. Ages ranged from 0.1 to 46 years, with a mean 9.2 years (SD 5.9 years). Atrial chambers were situs solitus in 88.9%, inversus in 11.2%. The ventriculoarterial connections were discordant in 28 (77.7%), double outlet right ventricle in 4 (11.1%) (one of them was a "criss cross" heart), single outlet (pulmonary atresia) in 4 (11.1%), and double outlet left ventricle in 1 (2.7%). Associated lesions: Ventricular septal defect with pulmonary stenosis or atresia was present in 21 (58%), ventricular septal defect with no pulmonary obstruction was observed in 10 (28%). Five had tricuspid regurgitation with right ventricular disfunction, (two adults). Surgical results: 22 (61%) required 28 surgical procedures: 8 (36%) were palliative and 19 (86%) were corrective, one of them was our first anatomical correction. Operative mortality in all was 40.1%, postoperative atrioventricular block was observed in 9 (40.1%).
Conclusion:
Right ventricular dysfunction is not uncommon. Surgical results revealed high mortality and high pacemaker requirement for atrioventricular block.
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