Ultrastructural findings in incontinentia pigmenti

From their ultrastructural study of incontinenti pigmenti, the authors confirm that in this condition there is no pigmentary anomaly, but that pigmentation is the last step of a still unknown process. At birth those who are affected display an intracellular edema which leads to the formation of a vesocobulla. In all 3 stages, the epidermis shows dyskeratotic cells and a transient pigmentary discharge.