Inflammatory linear verrucous epidermal nevus and arthritis: a new association
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S Al-Enezi1, A M Huber, B R Krafchik
1Division of Rheumatology, Hospital for Sick Children, University of Toronto, Toronto, Ontario, Canada.
The Journal of Pediatrics
|April 11, 2001
Insights
Inflammatory linear verrucous epidermal nevus (ILVEN) is a rare childhood skin condition. This study describes a new association between ILVEN and arthritis in two children, suggesting management strategies.
Area of Science:
- Dermatology
- Pediatrics
- Rheumatology
Background:
- Inflammatory linear verrucous epidermal nevus (ILVEN) is a rare, congenital skin disorder characterized by its linear, verrucous, and inflammatory nature.
- ILVEN typically presents in early childhood and can cause significant cosmetic and psychological distress.
Observation:
- This report details two pediatric cases presenting with concurrent ILVEN and arthritis.
- The co-occurrence of these conditions was previously undocumented in medical literature.
Findings:
- The study highlights a novel association between ILVEN and arthritis in pediatric patients.
- Clinical and diagnostic observations suggest a potential link warranting further investigation.
Implications:
- This finding expands the understanding of ILVEN's potential systemic manifestations.
- Early recognition and appropriate management of arthritis in children with ILVEN are crucial for improving patient outcomes.
Abstract:
Inflammatory linear verrucous epidermal nevus (ILVEN) is a rare, chronic skin condition that begins in early childhood. We present two children with ILVEN and arthritis, a previously undescribed association. We discuss the relevance of this association and suggest appropriate management for this arthritis.
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