Related Experiment Video
Updated: Jan 14, 2026
04:56
Modified Octopus Technique for Thoracoabdominal Aortic Aneurysm
Published on: August 1, 2025
467
A rare form of interrupted aortic arch
G Agnoletti1, A Borghi, F Annecchino
1Division of Cardiology, Ospedali Riuniti, Bergamo, Italy. gabriellaagnoletti@libero.it
Summary
This case study details a newborn with DiGeorge syndrome and complex aortic arch anomalies, including interrupted aortic arch type C. Surgical interventions like Norwood palliation were performed, with further procedures planned for biventricular correction.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Disease
- Medical Genetics
Background:
- DiGeorge syndrome is associated with a spectrum of congenital anomalies.
- Complex aortic arch abnormalities present significant surgical challenges in neonates.
Observation:
- A newborn presented with DiGeorge syndrome, aortic atresia, interrupted aortic arch type C, persistent right ventral aorta, and aberrant right innominate artery.
- The infant underwent staged surgical palliation, including Norwood procedure and bidirectional cavopulmonary anastomosis.
Findings:
- The case highlights the intricate management of severe congenital heart defects in DiGeorge syndrome.
- Surgical interventions aimed to reroute blood flow and prepare for eventual biventricular repair.
Implications:
- This case underscores the importance of early diagnosis and multidisciplinary management for complex congenital heart disease.
- Successful staged palliation offers a pathway towards definitive surgical correction in challenging pediatric cases.
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