Clear cell sarcoma of the kidney metastatic to jaw: case report

A case of an 8 year-old boy with history of nephroblastoma (Wilms' tumor) three years prior, which was managed with nephrectomy, chemotherapy and radiotherapy, is presented. During a routine follow up, a three month old rapidly growing mass on the left side of the face was detected. The roentgenogram showed a lytic lesion in the body and ascending ramus of the left jaw. Re-evaluation of the previous renal tumor was interpreted as a clear cell sarcoma of the kidney. Biopsy of the lesion of the left jaw showed similar histology, therefore, the diagnosis of clear cell sarcoma of the kidney metastatic to the left jaw was rendered. This is a rare case and to our knowledge is the first in the world's literature. We emphasize the diagnostic challenge of both the primary neoplasm and the metastasis and discuss the differential diagnosis of primary and metastatic sarcomas.