Related Experiment Videos

Delayed recognition of haemodynamically relevant congenital heart disease

J P Pfammatter1, F P Stocker

  • 1Department of Paediatric Cardiology, University Children's Hospital, 3010 Berne, Switzerland. Jean.Pierre.Pfammatter@insel.ch

Insights

Delayed diagnosis of congenital heart defects affects 10% of pediatric patients. Early recognition is crucial, as other cardiac findings besides murmurs were present in delayed cases, indicating missed diagnostic opportunities.

Area of Science:

  • Pediatric Cardiology
  • Congenital Heart Disease Diagnosis
  • Medical Outcomes

Background:

  • Delayed recognition of congenital heart defects (CHDs) can negatively impact long-term outcomes in children.
  • Accurate and timely diagnosis is essential for effective management of pediatric heart conditions.

Purpose of the Study:

  • To determine the proportion of pediatric patients with delayed diagnosis of CHD within a large treatment cohort.
  • To identify clinical indicators present in cases of delayed CHD diagnosis.

Main Methods:

  • A prospective study was conducted over three years.
  • Evaluated 323 pediatric patients requiring surgical or catheter intervention for CHD.
  • Examined patients with delayed diagnosis for specific clinical cardiac findings beyond systolic murmurs.

Main Results:

  • 10% (32 out of 323) of pediatric patients experienced delayed diagnosis of their heart defects.
  • The rate of delayed diagnosis was similar for both cyanotic (7/72) and acyanotic (25/251) heart defects.
  • Seven patients with delayed diagnosis developed complications, but no mortality was linked to the delay.

Conclusions:

  • A significant percentage of pediatric patients undergoing intervention for heart disease were diagnosed late.
  • Clinical findings other than systolic murmurs were consistently observed in patients with delayed diagnoses, suggesting potential for earlier detection.
Abstract

Related Concept Videos