Common iliac artery aneurysm due to fibromuscular dysplasia in infants

N Kuwabara1, T Kuwahara, K Takahashi

  • 1Department of Pediatric Cardiology, Gifu Prefectural Hospital, Japan.

Insights

This study reports the first infant case of a large common iliac artery aneurysm caused by fibromuscular dysplasia (FMD). Surgical repair and medical management successfully controlled blood pressure.

Area of Science:

  • Vascular Surgery
  • Pediatric Cardiology
  • Histopathology

Background:

  • Fibromuscular dysplasia (FMD) is a rare non-atherosclerotic vascular disease.
  • Iliac artery aneurysms are uncommon in infants.
  • Renal artery stenosis is a known complication of FMD.

Observation:

  • A seven-month-old infant presented with a large right common iliac artery aneurysm and bilateral renal artery stenoses.
  • Surgical intervention involved interposing a Gore-Tex graft.
  • Histological analysis confirmed medial fibromuscular dysplasia in the aneurysmal wall.

Findings:

  • Successful surgical repair of the common iliac artery aneurysm.
  • Postoperative blood pressure was normalized with medical therapy.
  • This represents the first documented case of a common iliac artery aneurysm due to FMD in an infant.

Implications:

  • Highlights the potential for FMD to cause significant vascular abnormalities in infants.
  • Emphasizes the importance of considering FMD in pediatric patients with arterial aneurysms and stenoses.
  • Suggests that surgical and medical management can be effective in pediatric cases.

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