Retroperitoneal malignant peripheral nerve sheath tumor associated with scoliosis in neurofibromatosis
1Departments of Orthopedic Surgery and Radiology, Niigata University School of Medicine, Asahimachi 1-751, Niigata 951-8510, Japan.
Journal of Spinal Disorders
|June 5, 2001
Abstract:
Neurofibromatosis 1 is an autosomal dominant disorder characterized by distinctive clinical problems including scoliosis and malignant peripheral nerve sheath tumors. We present two cases of retroperitoneal malignant peripheral nerve sheath tumor associated with scoliosis in neurofibromatosis. Presence of spinal deformity resulted in delay of the diagnosis of the sarcoma.
