Limited Wegener's granulomatosis of the epididymis

A case is presented of Wegener's granulomatosis limited to the epididymis in a 32-year-old man. Tests for antineutrophils cytoplasmic antibodies were negative throughout. He showed excellent response to treatment with prednisolone, azathioprine and cotrimoxazole, following recurrence of his disease, after local complete excision. He remains free of disease 40 months after the discontinuation of all his treatment.