Infantile hemangioendothelioma

R C Parmar1, S B Bavdekar, S S Borwankar

  • 1Department of Pediatrics, Seth G.S. Medical College & K.E.M. Hospital, Parel, Mumbai-400 012, Maharashtra, India. rameshparmar@yaloo.com

Insights

Infantile hemangioendothelioma, a rare pediatric liver tumor, can present unusually in older infants. Surgical excision led to a full recovery with no recurrence in a 19-month-old patient.

Area of Science:

  • Pediatric Oncology
  • Hepatobiliary Surgery

Background:

  • Primary hepatic tumors are rare in children, representing 3% of pediatric neoplasms.
  • Infantile hemangioendothelioma is a benign hepatic tumor of mesenchymal origin, typically diagnosed before six months of age.

Observation:

  • This report details an atypical case of infantile hemangioendothelioma in a 19-month-old female.
  • The tumor exhibited an unusual presentation and progression for this age group.

Findings:

  • Diagnosis was confirmed through combined radiological and histopathological evaluation.
  • Surgical excision of the hepatic tumor resulted in an uneventful recovery.

Implications:

  • This case highlights the importance of considering infantile hemangioendothelioma even with atypical presentations in older infants.
  • Early diagnosis and surgical intervention can lead to favorable outcomes for pediatric liver tumors.

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