Management of Crigler-Najjar Syndrome type I

H A Al-Shurafa1, A F Bassas, D C Broering

  • 1Department of Hepatobiliary Surgery and Transplantation, University Hospital Hamburg-Eppendorf, Germany. al-shurafa@uke.uni-hamburg.de

Saudi Medical Journal
|June 27, 2001
PubMed
Summary

Crigler-Najjar Syndrome type I, a rare genetic disorder, is effectively treated with liver transplantation, preventing severe neurological damage. Orthotopic liver transplantation is considered the optimal surgical approach for this condition.

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