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Successful plasma therapy in hemolytic uremic syndrome with factor H deficiency
S Nathanson1, V Frémeaux-Bacchi, G Deschênes
1Service de Néphrologie Pédiatrique, Hĵpital Armand-Trousseau, Paris, France.
Pediatric Nephrology (Berlin, Germany)
|July 24, 2001
Abstract:
A patient with homozygous factor H deficiency presented with hemolytic uremic syndrome (HUS) at the age of 7 months. After a 2-year period of stability, renal failure and erythrocyte fragmentation recurred between the age of 3 and 4 years. Fresh frozen plasma infusions allowed renal function to be improved and erythrocyte fragmentation to be stopped. Withdrawal of plasma therapy led to a relapse of the biological signs of HUS.