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Simultaneous bilateral central retinal vein occlusion associated with anticardiolipin antibodies in leukemia

N A Al-Abdulla1, J T Thompson, S E LaBorwit

  • 1Krieger Eye Institute, Sinai Hospital, Baltimore, Maryland, USA.

Insights

This case report details a patient with leukemia who developed simultaneous bilateral central retinal vein occlusion. Increased anticardiolipin antibodies, not hyperviscosity, were implicated in this rare ocular complication.

Area of Science:

  • Ophthalmology
  • Hematology
  • Immunology

Background:

  • Central retinal vein occlusion (CRVO) is a significant cause of vision loss.
  • Leukemia is a known risk factor for vascular occlusive events, including CRVO.
  • Anticardiolipin antibodies are associated with hypercoagulable states and thrombosis.

Observation:

  • A 65-year-old male with chronic myelogenous leukemia presented with sudden vision loss.
  • He developed simultaneous bilateral nonischemic and subsequently nonperfused central retinal vein occlusion.
  • Neovascular glaucoma developed in the left eye, despite normal white blood cell and platelet counts and low serum viscosity.

Findings:

  • The patient exhibited elevated anticardiolipin antibodies.
  • This case demonstrates a rare instance of simultaneous bilateral CRVO in a leukemic patient.
  • The findings suggest anticardiolipin antibodies play a role in CRVO pathogenesis in leukemia, independent of hyperviscosity.

Implications:

  • This case highlights a potential autoimmune mechanism contributing to CRVO in leukemia.
  • Ophthalmologists and hematologists should consider screening for anticardiolipin antibodies in leukemic patients with CRVO.
  • Further research is warranted to elucidate the precise mechanisms linking leukemia, anticardiolipin antibodies, and retinal vascular events.
Abstract

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