Primary transanal rectosigmoidectomy for Hirschsprung's disease: Preliminary results in the initial 33 cases

Y Gao1, G Li, X Zhang

  • 1Department of Pediatric Surgery, The Second Hospital of Xi'an Jiaotong University, Xi'an, P.R. China.

Insights

This study introduces a new transanal rectosigmoidectomy for Hirschsprung

Area of Science:

  • Pediatric Surgery
  • Gastroenterology
  • Surgical Innovation

Background:

  • Hirschsprung's disease (HD) is a congenital condition characterized by the absence of ganglion cells in the distal bowel.
  • Current surgical treatments for HD aim to remove the affected aganglionic segment and restore bowel continuity.
  • Minimally invasive techniques are increasingly explored to improve outcomes in pediatric surgical patients.

Purpose of the Study:

  • To describe a novel primary transanal rectosigmoidectomy technique for Hirschsprung's disease.
  • To present the preliminary surgical outcomes of this new procedure in neonates and infants.

Main Methods:

  • A cohort of 34 patients with biopsy-proven rectosigmoid HD underwent the transanal rectosigmoidectomy.
  • The procedure involved rectal mucosectomy, resection of the rectal muscular sleeve, partial internal sphincterotomy, and oblique anastomosis.
  • Patient data including operative time, bowel resection length, and postoperative complications were collected.

Main Results:

  • The mean operative time was 160 minutes, with an average bowel resection of 29.5 cm.
  • Postoperative enterocolitis (EC) occurred in 6.06% of patients, with successful management via rectal irrigation/dilation or myectomy.
  • During a 6- to 18-month follow-up, 84% of patients experienced 1 to 6 daily bowel movements.

Conclusions:

  • Primary transanal rectosigmoidectomy is a viable surgical approach for Hirschsprung's disease.
  • The technique demonstrates promising early results in neonates and infants.
  • Long-term follow-up is necessary to fully assess functional bowel outcomes.
Abstract