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Large demyelinating brain lesion mimicking a herniating tumor
B Censori1, C Agostinis, T Partziguian
1UO Neurology 2, Ospedali Riuniti, Bergamo, Italy.
Summary
A rare brain lesion mimicking a tumor, characterized by massive demyelination, required surgical removal due to rapid progression despite steroids. Early recognition via advanced imaging can prevent unnecessary surgery.
Area of Science:
- Neurology
- Neuro-oncology
- Pathology
Background:
- Brain lesions can present with complex imaging and clinical features.
- Differentiating between neoplastic and non-neoplastic conditions is crucial for appropriate management.
Observation:
- A large brain lesion with computed tomography (CT) findings suggestive of a herniating tumor was observed.
- The patient rapidly deteriorated, progressing to coma within six days despite high-dose steroid therapy.
Findings:
- Histological analysis revealed massive demyelination with preserved axons, ruling out a tumor.
- No recurrence was noted during a 55-month follow-up period post-excision.
Implications:
- Advanced neuroimaging techniques like magnetic resonance imaging (MRI) and spectroscopy can aid in early diagnosis.
- While non-invasive methods are preferred, surgical resection remains a critical option for rapidly progressing demyelinating lesions unresponsive to medical treatment.